Pruriginosa Pattern of Dystrophic Epidermolisys Bullosa: Clinical Case
نویسندگان
چکیده
Background. Epidermolisys bullosa pruriginosa is a rare pattern of dystrophic epidermolisys and characterized by severe itching that accompanies the formation papules, plaques nodes primarily on lower limbs skin imitating prurigo nodularis. Nowadays, less than 100 cases this disease are reported in world, thus, presentation clinical case relevant. Clinical description . The authors describe pruriginous dominant bullous epidermolysis 14-year-old female patient. Conclusion. Diagnosis extremely difficult currently all treatment limited to symptomatic therapy order stop prevent scarring.
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ژورنال
عنوان ژورنال: ?????????????? ????????????
سال: 2023
ISSN: ['1727-5776', '2500-3089']
DOI: https://doi.org/10.15690/pf.v19i6.2476